Type | Gene | Current/Channel Type |
---|---|---|
LQT1 | KCNQ1 (KvLQT1) | Component of slowly inactivating delayed rectifier IKs |
LQT2 | hERG | Delayed rectifier IKr rapidly inactivating cardiac Na+ channel |
LQT3 | SCN5A | |
LQT4 | Chromosome 4q25-27 | Subunit involved in regulation of cardiac repolarization? |
LQT5 | KCNE1 (MinK) | Component of IKs |
LQT6 | MiRP1 | Component of IKr |